Situs  Solitus: Systemic right atrium is on the right with a right –sided  trilobed lung, liver,gall bladder, and inferior vena cava. The pulmonary atrium is on the left with a left-sided bilobed lung, stomach, single spleen and aorta. The cardiac apex is on the left.

The incidence of congenital heart disease in patients with situs solitus and levocardia is only 0.6%-0.8%.

Situs Inversus: Mirror image of situs solitus

Seen in 0.01% of the population.

  The incidence of congenital heart disease- 3%-5%.

Situs Inversus with levocardia is rare and is almost always associated with congenital heart disease.

Kartagener syndrome is present in 20% of all patients with situs inversus.

Fifty percent of patients with immotile cilia syndrome have situs solitus and 50% have situs inversus.

Situs ambiguous or Heterotaxy- visceral malposition and dysmorphism associated with indeterminate atrial arrangement.

Subclassified into:

Asplenia syndrome-bilateral right sidedness, right isomerism or Ivemark syndrome

Polysplenia-bilateral left sidedness left isomerism

The incidence of congenital heart disease in patients with heterotaxy is very high, ranging from 50% to nearly 100%.

The present patient is being investigated for Kartagener syndrome.

Take Home Message:

TRIAD in Kartagener syndrome

Situs Inversus

Sinusitis

Bronchiectasis