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Answer to Case of the Week: Apr 1-Apr 8, 2010

1 year old presents with stridor


 



Same lesion can be seen elsewhere and can be associated with syndrome.

Asymmetric subglottic narrowing with loss of one shoulder

Diagnosis: Subglottic Hemangioma

Subglottic hemangioma posterior lateral position is most common and left >right, rarely calcify.

 

Hemangiomas arises by endothelial hyperplasia whereas vascular malformations arise by dysmorphogenesis and exhibit normal endothelial turnover.

 

Subglottic hemangiomas -1.5% congenital anomalies of the larynx.

 

Cutaneous hemangiomas are seen in 50% of cases.

 

PHACE SYNDROME:

P-Posterior fossa brain malformation

H-Hemangiomas

A-Arterial anomalies

C-Coarctation of aorta, cardiac defects

E-Eye abnormalities

7% have subglottic hemangiomas

 

Kasabach-Merritt Syndrome-Rarely associated with subglottic hemangioma. Usually seen with hemangioendothelioma of liver and with thrombocytopenia.

 

Differential Diagnosis:

Subglottic stenosis

Tracheal granuloma

Viral croup

Membranous croup

Tracheal papillomatosis

 

Treatment;

Conservative monitoring

Steroids

Co2 laser therapy

Laryngotracheoplasty

Interferon

Vincristine

Direct excision of subglottic hemangioma

 

Take Home Message:

In croup  there is symmetrical narrowing with loss of shoulders on both sides(Steepel Sign)

In subglottic hemangioma loss of shouder on one side.( See the figure and line drawing)

  

Residents Submitting Correct Diagnosis - Case of the Week
Radiology
Pediatrics
VCU Resident
  • Jeremy Camden
  • Todd Berry
  • Shep Morano
  • Joseph Eason
  • Brian Deuell
    Others
  • Brian TrottaUnited States of America
  • Bradley SpielerUnited States of America
  • Nicole KelleherUnited States of America
  • Wael NemattallaEgypt
  • JAMAL ABAZIDSyrian Arab Republic
  • Matthew ChaneyUnited States of America
  • BOB WONGCanada
  • Robert PalmerUnited States of America
  • John KirkhamUnited States of America
  • Anup GuptaIndia
  • Mark BittmanUnited States of America
  • Jason AllenUnited States of America
  • Christopher FrancisUnited States of America
  • Rajesh SIndia

    Disclaimer: This information is intended solely for resident review of presented cases which may or may not be pathologically proven. Information is derived from a number of published sources of varying reliability and does not represent original research from the institution. It is not intended to be comprehensive and should therefore not substitute for careful review of the literature.