Bleeding in the scalp, retroperitoneum, ankle joint with cystic changes in the bone, into small bowel and into the retropharyngeal space and all are male patients.
Hemophilia A- x-linked recessive bleeding disorder resulting from deficiency of VIII.
Incidence: 1 in 10,000 males in US.
Hemophilia B- Christmas disease from deficiency of factor IX.
Incidence: 1 in 100,000.
Hemophilia C- Rare in US and lack of clotting factor XI.
The symptoms are mild and can occur in boys and girls.
Hemearthrosis occur in 70-90% of patients.
50% of patients develop arthropathy.
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Pseudotumor occurs in 1-2% of patients with severe hemophilia ( clotting factor level <1% of factor VIII)